PDB ID 1x7z sequence information (FASTA format)
RELATED PDB ID 1u5b , 1x7w , 1x7x , 1x7y , 1x80
Descriptor Crystal structure of the human mitochondrial branched-chain alpha-ketoacid dehydrogenase
Title Crystal structure of the human mitochondrial branched-chain alpha-ketoacid dehydrogenase
Functional Keywords OXIDOREDUCTASE,KETOACID DEHYDROGENASE, BRANCHED-CHAIN, MULTI-ENZYME COMPLEX, ACYLATION, OXIDATIVE DECARBOXYLATION MAPLE SYRUP URINE DISEASE, THIAMIN DIPHOSPHATE, PHOSPHORYLATION, FLAVOPROTEIN
Biological source Homo sapiens
(human)
Cellular location
[UNP - P12694 ]
Mitochondrion matrix
Organ source
[UNP - P12694 ]
Bone marrow, and LungUNP - P12694 ]
LiverUNP - P12694 ]
EpitheliumUNP - P12694 ]
PlateletUNP - P21953 ]
PlacentaUNP - P21953 ]
Eye
Total number of polymer chains 2
Total molecular weight 84187.1 (the details in Structural Details Page )
Authors Wynn, R.M. , Kato, M. , Machius, M. , Chuang, J.L. , Li, J. , Tomchick, D.R. , Chuang, D.T.
(deposition date : 2004-08-16, release date : 2004-11-23)
Primary citation Wynn, R.M. , Kato, M. , Machius, M. , Chuang, J.L. , Li, J. , Tomchick, D.R. , Chuang, D.T.Structure ,
12:2185 - 2196, 2004.(PubMed : 15576032) (DOI: 10.1016/j.str.2004.09.013)
Experimental method X-RAY DIFFRACTION ( 1.72[Å] )
Other Database Information
